Movement Disorders (revue)

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Progressive supranuclear palsy‐like phenotype associated with bilateral hypoxic–ischemic striopallidal lesions

Identifieur interne : 003775 ( Main/Exploration ); précédent : 003774; suivant : 003776

Progressive supranuclear palsy‐like phenotype associated with bilateral hypoxic–ischemic striopallidal lesions

Auteurs : Hee Tae Kim [Royaume-Uni] ; Simon Shields [Royaume-Uni] ; Kailash P. Bhatia [Royaume-Uni] ; Niall Quinn [Royaume-Uni]

Source :

RBID : ISTEX:FBCAFC790077DF0A557A01DF7F013FC53904BF52

English descriptors

Abstract

A progressive supranuclear palsy (PSP)‐like syndrome due to vascular or anoxic brain insult is rare. We describe a 65‐year‐old man with a progressive PSP‐like phenotype associated with hypoxic–ischemic bilateral striopallidal lesions, secondary to rupture of and subsequent surgery for a thoracic aortic aneurysm. After early extrapyramidal features, 10 months later he started to fall, and developed levator inhibition. A supranuclear gaze palsy for downgaze was documented 5.5 years after the insult. © 2005 Movement Disorder Society

Url:
DOI: 10.1002/mds.20407


Affiliations:


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Le document en format XML

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<div type="abstract" xml:lang="en">A progressive supranuclear palsy (PSP)‐like syndrome due to vascular or anoxic brain insult is rare. We describe a 65‐year‐old man with a progressive PSP‐like phenotype associated with hypoxic–ischemic bilateral striopallidal lesions, secondary to rupture of and subsequent surgery for a thoracic aortic aneurysm. After early extrapyramidal features, 10 months later he started to fall, and developed levator inhibition. A supranuclear gaze palsy for downgaze was documented 5.5 years after the insult. © 2005 Movement Disorder Society</div>
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